Airway management in Escobar syndrome

A formidable challenge

Shaji Mathew, Souvik Chaudhuri, H. D. Arun Kumar, Tim Thomas Joseph

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Escobar syndrome is a rare autosomal recessive disorder characterized by flexion joint and digit contractures, skin webbing, cleft palate, deformity of spine and cervical spine fusion. Associated difficult airway is mainly due to micrognathia, retrognathia, webbing of neck and limitation of the mouth opening and neck extension. We report a case of a 1 year old child with Escobar syndrome posted for bilateral hamstrings to quadriceps transfer. The child had adequate mouth opening with no evidence of cervical spine fusion, yet we faced difficulty in intubation which was ultimately overcome by securing a proseal laryngeal mask airway (PLMA) and then by intubating with an endotracheal tube railroaded over a paediatric fibreoptic bronchoscope passed through the lumen of a PLMA.

Original languageEnglish
Pages (from-to)603-605
Number of pages3
JournalIndian Journal of Anaesthesia
Volume57
Issue number6
DOIs
Publication statusPublished - 11-2013
Externally publishedYes

Fingerprint

Airway Management
Laryngeal Masks
Spine
Micrognathism
Mouth
Neck
Retrognathia
Bronchoscopes
Cleft Palate
Contracture
Intubation
Joints
Pediatrics
Skin
Multiple pterygium syndrome

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

Cite this

Mathew, S., Chaudhuri, S., Arun Kumar, H. D., & Joseph, T. T. (2013). Airway management in Escobar syndrome: A formidable challenge. Indian Journal of Anaesthesia, 57(6), 603-605. https://doi.org/10.4103/0019-5049.123336
Mathew, Shaji ; Chaudhuri, Souvik ; Arun Kumar, H. D. ; Joseph, Tim Thomas. / Airway management in Escobar syndrome : A formidable challenge. In: Indian Journal of Anaesthesia. 2013 ; Vol. 57, No. 6. pp. 603-605.
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Mathew, S, Chaudhuri, S, Arun Kumar, HD & Joseph, TT 2013, 'Airway management in Escobar syndrome: A formidable challenge', Indian Journal of Anaesthesia, vol. 57, no. 6, pp. 603-605. https://doi.org/10.4103/0019-5049.123336

Airway management in Escobar syndrome : A formidable challenge. / Mathew, Shaji; Chaudhuri, Souvik; Arun Kumar, H. D.; Joseph, Tim Thomas.

In: Indian Journal of Anaesthesia, Vol. 57, No. 6, 11.2013, p. 603-605.

Research output: Contribution to journalArticle

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