Anaesthesia for left thoracoscopic sympathectomy for refractory long QT syndrome: Three case reports

Madhusudan Upadya, Julie C.R. Misquith, Rammoorthi Rao

Research output: Contribution to journalArticle

3 Citations (Scopus)

Abstract

Congenital long QT syndrome (LQTS) is a rare genetic disorder that has been associated with various genetic mutations including life-threatening cardiac arrhythmias and sudden death. Left thoracoscopic sympathectomy is an effective treatment for patients who are refractory to medical therapy or who need frequent epicardial internal cardio defibrillator intervention. The authors report three cases, one adult and two children, who underwent successful left thoracoscopic sympathectomy. All three patients remained clinically stable without arrhythmias through 3 months of follow-up. It is suggested in the literature that 77% of patients experienced immediate relief of symptoms. The results of this case report suggest that left thoracoscopic sympathectomy is a safe and effective approach for treating patients with LQTS.

Original languageEnglish
Pages (from-to)156-159
Number of pages4
JournalSouthern African Journal of Anaesthesia and Analgesia
Volume22
Issue number5
DOIs
Publication statusPublished - 01-01-2016

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Long QT Syndrome
Sympathectomy
Anesthesia
Cardiac Arrhythmias
Inborn Genetic Diseases
Defibrillators
Sudden Death
Mutation
Therapeutics

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

Cite this

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Anaesthesia for left thoracoscopic sympathectomy for refractory long QT syndrome : Three case reports. / Upadya, Madhusudan; Misquith, Julie C.R.; Rao, Rammoorthi.

In: Southern African Journal of Anaesthesia and Analgesia, Vol. 22, No. 5, 01.01.2016, p. 156-159.

Research output: Contribution to journalArticle

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