Congenital cystic adenomatoid malformation of lung type 1

Alka Mary Mathai, Hema Kini, Muktha R. Pai, Ashok B. Shetty, Nirupama Murali

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

Congenital cystic adenomatoid malformation, a rare developmental, hamartomatous abnormality of the lung, usually is unilateral, is localized, and presents in early infancy. Delayed occurrence in older children and multilobar involvement are rare. We describe a case of congenital cystic adenomatoid malformation type 1 with multilobar involvement, associated emphysema, and coexistent tracheobronchopathia osteochondroplastica in an adolescent girl for whom the correct diagnosis was achieved only on histologic examination. The importance of an accurate diagnosis of this entity enables proper subtyping, management to minimize the risk of infections and malignancy, and exclusion of associated malformations.

Original languageEnglish
JournalJournal of Pediatric Surgery
Volume45
Issue number2
DOIs
Publication statusPublished - 01-02-2010

Fingerprint

Congenital Cystic Adenomatoid Malformation of Lung
Emphysema
Lung
Infection
Neoplasms

All Science Journal Classification (ASJC) codes

  • Surgery
  • Pediatrics, Perinatology, and Child Health

Cite this

Mathai, Alka Mary ; Kini, Hema ; Pai, Muktha R. ; Shetty, Ashok B. ; Murali, Nirupama. / Congenital cystic adenomatoid malformation of lung type 1. In: Journal of Pediatric Surgery. 2010 ; Vol. 45, No. 2.
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Congenital cystic adenomatoid malformation of lung type 1. / Mathai, Alka Mary; Kini, Hema; Pai, Muktha R.; Shetty, Ashok B.; Murali, Nirupama.

In: Journal of Pediatric Surgery, Vol. 45, No. 2, 01.02.2010.

Research output: Contribution to journalArticle

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AU - Mathai, Alka Mary

AU - Kini, Hema

AU - Pai, Muktha R.

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AB - Congenital cystic adenomatoid malformation, a rare developmental, hamartomatous abnormality of the lung, usually is unilateral, is localized, and presents in early infancy. Delayed occurrence in older children and multilobar involvement are rare. We describe a case of congenital cystic adenomatoid malformation type 1 with multilobar involvement, associated emphysema, and coexistent tracheobronchopathia osteochondroplastica in an adolescent girl for whom the correct diagnosis was achieved only on histologic examination. The importance of an accurate diagnosis of this entity enables proper subtyping, management to minimize the risk of infections and malignancy, and exclusion of associated malformations.

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