Management of dextro-transposition of the great arteries with intact interventricular septum along with regression of the left ventricle remains a challenge. Atrial switch always raises concerns about the fate of the right ventricle as a systemic ventricle in the long run. A two-stage repair with pulmonary artery banding and a modified Blalock-Taussig shunt or a single-stage arterial switch with mechanical support has a higher mortality and morbidity. This report describes a case of a 3-year-old girl with dextro-transposition of the great arteries with intact interventricular septum that was managed by a Damus-Kaye-Stansel procedure with a right bidirectional cavopulmonary anastomosis in the first stage to train the left ventricle, followed by a definitive operation (arterial switch) in the second stage.
All Science Journal Classification (ASJC) codes
- Pulmonary and Respiratory Medicine
- Cardiology and Cardiovascular Medicine