Enteropathy associated t cell lymphoma – A case report of an uncommon extranodal t cell lymphoma

V. Geetha, Ranjini Kudva, Anna Joseph Amprayil

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Enteropathy associated T cell lymphoma is a rare primary intestinal lymphoma. It is often, but not always associated with celiac disease. Intraepithelial T cells are postulated as the cell of origin. It is a rare disease accounting for fewer than 5% of all gastrointestinal tract lymphomas. Recent studies indicate that EATL consists of two diseases that are morphologically and genetically distinct and differ with respect to their frequency of association with celiac disease. Current WHO classification recognises two subtypes of EATL – type 1 (classic) and type 2, based on morphology and immunophenotype. EATL type 1 is a large cell lymphoma which is more common and is more commonly associated with celiac disease compared to type 2. Most common site of involvement is the small intestine. We report a case of EATL type 1, in a 62-year-old female patient who presented with features of intestinal obstruction. However, she did not have spruce like featutes.

Original languageEnglish
Pages (from-to)FD10-FD12
JournalJournal of Clinical and Diagnostic Research
Volume8
Issue number10
DOIs
Publication statusPublished - 01-01-2014

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Celiac Disease
Lymphoma
Enteropathy-Associated T-Cell Lymphoma
T-cells
Intestinal Obstruction
Rare Diseases
Small Intestine
Gastrointestinal Tract
T-Lymphocytes

All Science Journal Classification (ASJC) codes

  • Clinical Biochemistry

Cite this

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Enteropathy associated t cell lymphoma – A case report of an uncommon extranodal t cell lymphoma. / Geetha, V.; Kudva, Ranjini; Amprayil, Anna Joseph.

In: Journal of Clinical and Diagnostic Research, Vol. 8, No. 10, 01.01.2014, p. FD10-FD12.

Research output: Contribution to journalArticle

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