Epidermolysis Bullosa – An anaesthetic challenge

Lokvendra Singh Budania, M. V. Eeshwar, Vamshidhar Chamala Reddy, Yogesh K. Gaude, Sai Anand, Anshu Sharma

Research output: Contribution to journalArticle

Abstract

Epidermolysis bullosa (EB) is a rare genetic disorder characterized by blisters of skin and mucosa as a result of friction or minor trauma. EB can be of three forms: Epidermolysis Simplex (EBS), Junctional Epidermolysis Bullosa (JEB) and Dystrophic (DEB). Management of EB poses a challenge to the anaesthetist. We report a case of a 4-year-old girl who was diagnosed with DEB at birth. She was found to have an oesophageal stricture and was posted for balloon dilatation of the oesophagus. Airway examination revealed mouth opening of 1.5-2 fingers breadth with adequate neck movements. Difficult airway was anticipated. General anaesthesia was administered, and intubation was achieved using Airtraq video laryngoscope. Care was taken not to cause further trauma to the skin and mucosa in the perioperative period.

Original languageEnglish
Pages (from-to)163-165
Number of pages3
JournalSri Lankan Journal of Anaesthesiology
Volume27
Issue number2
DOIs
Publication statusPublished - 01-01-2019
Externally publishedYes

Fingerprint

Epidermolysis Bullosa
Anesthetics
Mucous Membrane
Junctional Epidermolysis Bullosa
Laryngoscopes
Esophageal Stenosis
Skin
Inborn Genetic Diseases
Perioperative Period
Friction
Wounds and Injuries
Blister
Intubation
General Anesthesia
Esophagus
Fingers
Mouth
Dilatation
Neck
Parturition

All Science Journal Classification (ASJC) codes

  • Anesthesiology and Pain Medicine

Cite this

Budania, L. S., Eeshwar, M. V., Reddy, V. C., Gaude, Y. K., Anand, S., & Sharma, A. (2019). Epidermolysis Bullosa – An anaesthetic challenge. Sri Lankan Journal of Anaesthesiology, 27(2), 163-165. https://doi.org/10.4038/slja.v27i2.8405
Budania, Lokvendra Singh ; Eeshwar, M. V. ; Reddy, Vamshidhar Chamala ; Gaude, Yogesh K. ; Anand, Sai ; Sharma, Anshu. / Epidermolysis Bullosa – An anaesthetic challenge. In: Sri Lankan Journal of Anaesthesiology. 2019 ; Vol. 27, No. 2. pp. 163-165.
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Budania, LS, Eeshwar, MV, Reddy, VC, Gaude, YK, Anand, S & Sharma, A 2019, 'Epidermolysis Bullosa – An anaesthetic challenge', Sri Lankan Journal of Anaesthesiology, vol. 27, no. 2, pp. 163-165. https://doi.org/10.4038/slja.v27i2.8405

Epidermolysis Bullosa – An anaesthetic challenge. / Budania, Lokvendra Singh; Eeshwar, M. V.; Reddy, Vamshidhar Chamala; Gaude, Yogesh K.; Anand, Sai; Sharma, Anshu.

In: Sri Lankan Journal of Anaesthesiology, Vol. 27, No. 2, 01.01.2019, p. 163-165.

Research output: Contribution to journalArticle

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Budania LS, Eeshwar MV, Reddy VC, Gaude YK, Anand S, Sharma A. Epidermolysis Bullosa – An anaesthetic challenge. Sri Lankan Journal of Anaesthesiology. 2019 Jan 1;27(2):163-165. https://doi.org/10.4038/slja.v27i2.8405