Low-grade adenocarcinoma of endolymphatic sac origin

Saurabh Malhotra, Ravikala V. Rao, Manna Valiathan, Mary Mathew, Deepak Ranjan Nayak, A. Raja

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

We present a case of papillary cystic low-grade adenocarcinoma of endolymphatic sac origin. These tumors are very rare and only a few cases have been reported in literature. They have a protracted clinical course causing progressive invasion and bony destruction. Radiologically, they appear as a heterogenous lobulated vascular mass, invading bone and compressing surrounding structures. Histologically, these tumors are composed of uniform population of cells, resembling normal endolymphatic sac epithelium. This causes considerable diagnostic difficulty. A strong index of suspicion along with clinical and radiological correlation is essential to arrive at a correct diagnosis. In some bilateral cases, association with von Hippel-Lindau disease has been noted. Radical mastoidectomy and temporal bone resection, which may sometimes necessitate sacrifice of cranial nerves, is the treatment of choice.

Original languageEnglish
Pages (from-to)362-365
Number of pages4
JournalAmerican Journal of Otolaryngology - Head and Neck Medicine and Surgery
Volume27
Issue number5
DOIs
Publication statusPublished - 01-09-2006

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Endolymphatic Sac
Adenocarcinoma
von Hippel-Lindau Disease
Cranial Nerves
Temporal Bone
Blood Vessels
Neoplasms
Epithelium
Bone and Bones
Population

All Science Journal Classification (ASJC) codes

  • Otorhinolaryngology

Cite this

Malhotra, Saurabh ; Rao, Ravikala V. ; Valiathan, Manna ; Mathew, Mary ; Nayak, Deepak Ranjan ; Raja, A. / Low-grade adenocarcinoma of endolymphatic sac origin. In: American Journal of Otolaryngology - Head and Neck Medicine and Surgery. 2006 ; Vol. 27, No. 5. pp. 362-365.
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Low-grade adenocarcinoma of endolymphatic sac origin. / Malhotra, Saurabh; Rao, Ravikala V.; Valiathan, Manna; Mathew, Mary; Nayak, Deepak Ranjan; Raja, A.

In: American Journal of Otolaryngology - Head and Neck Medicine and Surgery, Vol. 27, No. 5, 01.09.2006, p. 362-365.

Research output: Contribution to journalArticle

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