Role of interventional radiology in the diagnosis and management of congenital extrahepatic portosystemic shunts: Two case reports

Sheetal V. Mathai, Victor Kondray, Elias Salloum, Kamlesh Kukreja, Sidhartha Tavri

Research output: Contribution to journalArticle


Congenital extrahepatic portosystemic shunt (CEPS) is a rare splanchnic venous malformation, wherein the portal venous outflow drains into the systemic venous circulation via a pathologic shunt. CEPS exhibits heterogeneous clinical behavior and angiography is the gold standard for evaluation of the portomesenteric communication to systemic vasculature. The potential severity of complications necessitates shunt closure. Here, we present two cases of CEPS. The first patient presented with an asymptomatic hyperammonemia and was found to have a Type 1 CEPS with absence of intrahepatic portal system. The second patient was asymptomatic and was incidentally found to have a Type 2 CEPS on imaging with normal intrahepatic portal system. Both patients were successfully treated with endovascular occlusion of the CEPS.

Original languageEnglish
Pages (from-to)219-222
Number of pages4
JournalIndian Journal of Radiology and Imaging
Issue number2
Publication statusPublished - 01-04-2019
Externally publishedYes


All Science Journal Classification (ASJC) codes

  • Radiology Nuclear Medicine and imaging

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