Safe intubation in Morquio-Brailsford syndrome

A challenge for the anesthesiologist

Souvik Chaudhuri, Arun Kumar Handigodu Duggappa, Shaji Mathew, Sandeep Venkatesh

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Morquio-Brailsford syndrome is a type of mucopolysaccharidoses. It is a rare disease with features of short stature, atlantoaxial instability with risk of cord damage, odontoid hypoplasia, pectus carinatum, spine deformities, hepatomegaly, and restrictive lung disease. Neck movements during intubation are associated with the risk of quadriparesis due to cervical instability. This, along with the distortion of the airway anatomy due to deposition of mucopolysaccharides makes airway management arduous. We present our experience in management of difficult airway in a 3-year-old girl with Morquio-Brailsford syndrome posted for magnetic resonance imaging and computerized tomography scan of a suspected unstable cervical spine. As utmost sagacity during intubation is required, the child was intubated inside operation theatre in the presence of experienced anesthesiologists and then shifted to the peripheral location. Intubation was done with an endotracheal tube railroaded over a pediatric fibreoptic bronchoscope passed through the lumen of a classic laryngeal mask airway, keeping head in neutral position.

Original languageEnglish
Pages (from-to)258-261
Number of pages4
JournalJournal of Anaesthesiology Clinical Pharmacology
Volume29
Issue number2
DOIs
Publication statusPublished - 2013
Externally publishedYes

Fingerprint

Mucopolysaccharidosis IV
Intubation
Airway Management
Spine
Mucopolysaccharidosis I
Bronchoscopes
Laryngeal Masks
Quadriplegia
Hepatomegaly
Rare Diseases
Glycosaminoglycans
Lung Diseases
Anatomy
Neck
Head
Tomography
Magnetic Resonance Imaging
Pediatrics
Anesthesiologists

All Science Journal Classification (ASJC) codes

  • Pharmacology (medical)
  • Anesthesiology and Pain Medicine
  • Pharmacology, Toxicology and Pharmaceutics(all)

Cite this

Chaudhuri, Souvik ; Duggappa, Arun Kumar Handigodu ; Mathew, Shaji ; Venkatesh, Sandeep. / Safe intubation in Morquio-Brailsford syndrome : A challenge for the anesthesiologist. In: Journal of Anaesthesiology Clinical Pharmacology. 2013 ; Vol. 29, No. 2. pp. 258-261.
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Safe intubation in Morquio-Brailsford syndrome : A challenge for the anesthesiologist. / Chaudhuri, Souvik; Duggappa, Arun Kumar Handigodu; Mathew, Shaji; Venkatesh, Sandeep.

In: Journal of Anaesthesiology Clinical Pharmacology, Vol. 29, No. 2, 2013, p. 258-261.

Research output: Contribution to journalArticle

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